Obstrucción intestinal de debut tardío

  1. E. Cid París
  2. G. Galicia Poblet
  3. Gema Arriola Pereda
  4. M.E. Rubio Jiménez
  5. M. Pangua Gómez
  6. Ana Serrano González
  7. J. M. Jiménez Bustos
Revista:
Revista española de pediatría: clínica e investigación

ISSN: 0034-947X

Año de publicación: 2010

Volumen: 66

Número: 3

Páginas: 193-196

Tipo: Artículo

Otras publicaciones en: Revista española de pediatría: clínica e investigación

Resumen

Hirschsprung's disease is a congenital disorder of the colon in which certain nerve cells, known as ganglion cells, are absent, causing chronic constipation. A barium enema is the mainstay of diagnosis of Hirschsprung's, though a rectal biopsy showing the lack of ganglion cells is the only certain method of diagnosis. The usual treatment is excision of the aganglionic colon and "pull-through" surgery of ganglionic colon with a coloanal anastomosis. We report a case of Hirschsprung's disease with bowel obstruction in the infant period.

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