Obstrucción intestinal de debut tardío
- E. Cid París
- G. Galicia Poblet
- Gema Arriola Pereda
- M.E. Rubio Jiménez
- M. Pangua Gómez
- Ana Serrano González
- J. M. Jiménez Bustos
ISSN: 0034-947X
Año de publicación: 2010
Volumen: 66
Número: 3
Páginas: 193-196
Tipo: Artículo
Otras publicaciones en: Revista española de pediatría: clínica e investigación
Resumen
Hirschsprung's disease is a congenital disorder of the colon in which certain nerve cells, known as ganglion cells, are absent, causing chronic constipation. A barium enema is the mainstay of diagnosis of Hirschsprung's, though a rectal biopsy showing the lack of ganglion cells is the only certain method of diagnosis. The usual treatment is excision of the aganglionic colon and "pull-through" surgery of ganglionic colon with a coloanal anastomosis. We report a case of Hirschsprung's disease with bowel obstruction in the infant period.
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