Obstrucción intestinal de debut tardío

  1. E. Cid París
  2. G. Galicia Poblet
  3. Gema Arriola Pereda
  4. M.E. Rubio Jiménez
  5. M. Pangua Gómez
  6. Ana Serrano González
  7. J. M. Jiménez Bustos
Journal:
Revista española de pediatría: clínica e investigación

ISSN: 0034-947X

Year of publication: 2010

Volume: 66

Issue: 3

Pages: 193-196

Type: Article

SCOPUS: 2-s2.0-77953581660 DIALNET GOOGLE SCHOLAR

More publications in: Revista española de pediatría: clínica e investigación

Abstract

Hirschsprung's disease is a congenital disorder of the colon in which certain nerve cells, known as ganglion cells, are absent, causing chronic constipation. A barium enema is the mainstay of diagnosis of Hirschsprung's, though a rectal biopsy showing the lack of ganglion cells is the only certain method of diagnosis. The usual treatment is excision of the aganglionic colon and "pull-through" surgery of ganglionic colon with a coloanal anastomosis. We report a case of Hirschsprung's disease with bowel obstruction in the infant period.

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